Stanley Skopit and Ramya Garlapati*
Primary leptomeningeal melanoma is a rare and aggressive tumor of the CNS. They are much more common in patients with multiple congenital melanocytic nevi. Congenital melanocytic nevi (CMN) are commonly known as moles and are benign pigmented macules that are present at birth or appear within the first few months of life. We report a case of a 28-year-old male with multiple CMN, who was found to have a primary leptomeningeal melanoma. We present this case for its rarity and to review the current association between CMN and neurocutaneous melanosis.